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Imaging findings in Erdheim-Chester disease : what every radiologist needs to know
diabetes insipidus
neurogenic
Erdheim-Chester disease
histiocytosis
non-Langerhans cell
Bibliogr. s. e62
Erdheim-Chester disease (ECD) is a rare sporadic non-Langerhans cell histiocytic (LCH) proliferative disorder with systemic predilection. It usually affects adults in the 5th-7th decades of life and has non-specific clinical manifestations. Its suspicion is often heralded by the presence of characteristic radiological findings and subsequently confirmed by demonstration of CD68-positive xanthogranulomatous infiltrates on histopathology. Despite being a non-malignant entity, it might be fatal due to organ dysfunction. Imaging plays a key role in the diagnosis, management, and follow-up. Imaging findings are essential to establish the diagnosis, assess actual disease burden, and explore the aetiopathogenesis and therapeutic options to halt disease progression and associated morbidity.
dc.abstract.en | Erdheim-Chester disease (ECD) is a rare sporadic non-Langerhans cell histiocytic (LCH) proliferative disorder with systemic predilection. It usually affects adults in the 5th-7th decades of life and has non-specific clinical manifestations. Its suspicion is often heralded by the presence of characteristic radiological findings and subsequently confirmed by demonstration of CD68-positive xanthogranulomatous infiltrates on histopathology. Despite being a non-malignant entity, it might be fatal due to organ dysfunction. Imaging plays a key role in the diagnosis, management, and follow-up. Imaging findings are essential to establish the diagnosis, assess actual disease burden, and explore the aetiopathogenesis and therapeutic options to halt disease progression and associated morbidity. | pl |
dc.contributor.author | Kumar, Pawan | pl |
dc.contributor.author | Singh, Anuradha | pl |
dc.contributor.author | Gamanagatti, Shivanand | pl |
dc.contributor.author | Kumar, Sanjeev | pl |
dc.contributor.author | Chandrashekhara, Sheragaru Hanumanthappa | pl |
dc.date.accessioned | 2018-02-06T13:32:54Z | |
dc.date.available | 2018-02-06T13:32:54Z | |
dc.date.issued | 2018 | pl |
dc.date.openaccess | 0 | |
dc.description.accesstime | w momencie opublikowania | |
dc.description.additional | Bibliogr. s. e62 | pl |
dc.description.physical | e54-e62 | pl |
dc.description.version | ostateczna wersja wydawcy | |
dc.description.volume | 83 | pl |
dc.identifier.doi | 10.5114/pjr.2018.73290 | pl |
dc.identifier.eissn | 1899-0967 | pl |
dc.identifier.issn | 1733-134X | pl |
dc.identifier.uri | https://ruj.uj.edu.pl/xmlui/handle/item/49791 | |
dc.language | eng | pl |
dc.language.container | eng | pl |
dc.rights | Udzielam licencji. Uznanie autorstwa - Użycie niekomercyjne - Bez utworów zależnych 3.0 Polska | * |
dc.rights.licence | CC-BY-NC-ND | |
dc.rights.uri | http://creativecommons.org/licenses/by-nc-nd/3.0/pl/legalcode | * |
dc.share.type | otwarte czasopismo | |
dc.subject.en | diabetes insipidus | pl |
dc.subject.en | neurogenic | pl |
dc.subject.en | Erdheim-Chester disease | pl |
dc.subject.en | histiocytosis | pl |
dc.subject.en | non-Langerhans cell | pl |
dc.subtype | ReviewArticle | pl |
dc.title | Imaging findings in Erdheim-Chester disease : what every radiologist needs to know | pl |
dc.title.journal | Polish Journal of Radiology | pl |
dc.type | JournalArticle | pl |
dspace.entity.type | Publication |
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