Imaging findings in Erdheim-Chester disease : what every radiologist needs to know

2018
journal article
review article
39
dc.abstract.enErdheim-Chester disease (ECD) is a rare sporadic non-Langerhans cell histiocytic (LCH) proliferative disorder with systemic predilection. It usually affects adults in the 5th-7th decades of life and has non-specific clinical manifestations. Its suspicion is often heralded by the presence of characteristic radiological findings and subsequently confirmed by demonstration of CD68-positive xanthogranulomatous infiltrates on histopathology. Despite being a non-malignant entity, it might be fatal due to organ dysfunction. Imaging plays a key role in the diagnosis, management, and follow-up. Imaging findings are essential to establish the diagnosis, assess actual disease burden, and explore the aetiopathogenesis and therapeutic options to halt disease progression and associated morbidity.pl
dc.contributor.authorKumar, Pawanpl
dc.contributor.authorSingh, Anuradhapl
dc.contributor.authorGamanagatti, Shivanandpl
dc.contributor.authorKumar, Sanjeevpl
dc.contributor.authorChandrashekhara, Sheragaru Hanumanthappapl
dc.date.accessioned2018-02-06T13:32:54Z
dc.date.available2018-02-06T13:32:54Z
dc.date.issued2018pl
dc.date.openaccess0
dc.description.accesstimew momencie opublikowania
dc.description.additionalBibliogr. s. e62pl
dc.description.physicale54-e62pl
dc.description.versionostateczna wersja wydawcy
dc.description.volume83pl
dc.identifier.doi10.5114/pjr.2018.73290pl
dc.identifier.eissn1899-0967pl
dc.identifier.issn1733-134Xpl
dc.identifier.urihttps://ruj.uj.edu.pl/xmlui/handle/item/49791
dc.languageengpl
dc.language.containerengpl
dc.rightsUdzielam licencji. Uznanie autorstwa - Użycie niekomercyjne - Bez utworów zależnych 3.0 Polska*
dc.rights.licenceCC-BY-NC-ND
dc.rights.urihttp://creativecommons.org/licenses/by-nc-nd/3.0/pl/legalcode*
dc.share.typeotwarte czasopismo
dc.subject.endiabetes insipiduspl
dc.subject.enneurogenicpl
dc.subject.enErdheim-Chester diseasepl
dc.subject.enhistiocytosispl
dc.subject.ennon-Langerhans cellpl
dc.subtypeReviewArticlepl
dc.titleImaging findings in Erdheim-Chester disease : what every radiologist needs to knowpl
dc.title.journalPolish Journal of Radiologypl
dc.typeJournalArticlepl
dspace.entity.typePublication
dc.abstract.enpl
Erdheim-Chester disease (ECD) is a rare sporadic non-Langerhans cell histiocytic (LCH) proliferative disorder with systemic predilection. It usually affects adults in the 5th-7th decades of life and has non-specific clinical manifestations. Its suspicion is often heralded by the presence of characteristic radiological findings and subsequently confirmed by demonstration of CD68-positive xanthogranulomatous infiltrates on histopathology. Despite being a non-malignant entity, it might be fatal due to organ dysfunction. Imaging plays a key role in the diagnosis, management, and follow-up. Imaging findings are essential to establish the diagnosis, assess actual disease burden, and explore the aetiopathogenesis and therapeutic options to halt disease progression and associated morbidity.
dc.contributor.authorpl
Kumar, Pawan
dc.contributor.authorpl
Singh, Anuradha
dc.contributor.authorpl
Gamanagatti, Shivanand
dc.contributor.authorpl
Kumar, Sanjeev
dc.contributor.authorpl
Chandrashekhara, Sheragaru Hanumanthappa
dc.date.accessioned
2018-02-06T13:32:54Z
dc.date.available
2018-02-06T13:32:54Z
dc.date.issuedpl
2018
dc.date.openaccess
0
dc.description.accesstime
w momencie opublikowania
dc.description.additionalpl
Bibliogr. s. e62
dc.description.physicalpl
e54-e62
dc.description.version
ostateczna wersja wydawcy
dc.description.volumepl
83
dc.identifier.doipl
10.5114/pjr.2018.73290
dc.identifier.eissnpl
1899-0967
dc.identifier.issnpl
1733-134X
dc.identifier.uri
https://ruj.uj.edu.pl/xmlui/handle/item/49791
dc.languagepl
eng
dc.language.containerpl
eng
dc.rights*
Udzielam licencji. Uznanie autorstwa - Użycie niekomercyjne - Bez utworów zależnych 3.0 Polska
dc.rights.licence
CC-BY-NC-ND
dc.rights.uri*
http://creativecommons.org/licenses/by-nc-nd/3.0/pl/legalcode
dc.share.type
otwarte czasopismo
dc.subject.enpl
diabetes insipidus
dc.subject.enpl
neurogenic
dc.subject.enpl
Erdheim-Chester disease
dc.subject.enpl
histiocytosis
dc.subject.enpl
non-Langerhans cell
dc.subtypepl
ReviewArticle
dc.titlepl
Imaging findings in Erdheim-Chester disease : what every radiologist needs to know
dc.title.journalpl
Polish Journal of Radiology
dc.typepl
JournalArticle
dspace.entity.type
Publication
Affiliations

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