Endolymphatic sac tumour (ELST). Case report of a rare tumour of the temporal bone, presenting as a mass in a cerebello-pontine angle

2013
journal article
article
cris.lastimport.wos2024-04-10T00:14:37Z
dc.abstract.enEndolymphatic sac tumour (ELST) is a primary low-grade, locally invasive adenocarcinoma of the endolymphatic sac, characterized by the proliferation of cuboidal cells forming a papillotubular pattern and colloid-filled cysts. Rare in the general population, it coincides significantly with the presence of von Hippel-Lindau disease. The natural history, mechanisms underlying the early symptoms, anatomical origin of ELST and optimal timing of their treatment are unknown. In this study, we report a Polish male patient with sporadic ELST (without a family history of VHL disease) along with a review of literature. The light microscopic and immunohistochemical features as well as clinical presentation were typical of ELST.pl
dc.affiliationWydział Lekarski : Zakład Patomorfologii Klinicznej i Doświadczalnejpl
dc.affiliationWydział Lekarski : Zakład Neuropatologiipl
dc.cm.date2020-01-07
dc.cm.id58981
dc.contributor.authorCzopek, Jacek - 129116 pl
dc.contributor.authorWaśko, Marcinpl
dc.contributor.authorAdamek, Dariusz - 128411 pl
dc.date.accessioned2020-01-17T07:51:52Z
dc.date.available2020-01-17T07:51:52Z
dc.date.issued2013pl
dc.date.openaccess0
dc.description.accesstimew momencie opublikowania
dc.description.number2pl
dc.description.physical164-168pl
dc.description.points15pl
dc.description.versionostateczna wersja wydawcy
dc.description.volume51pl
dc.identifier.doi10.5114/fn.2013.35960pl
dc.identifier.eissn1509-572Xpl
dc.identifier.issn1641-4640pl
dc.identifier.projectROD UJ / OPpl
dc.identifier.urihttps://ruj.uj.edu.pl/xmlui/handle/item/131556
dc.languageengpl
dc.language.containerengpl
dc.rightsUdzielam licencji. Uznanie autorstwa - Użycie niekomercyjne - Na tych samych warunkach 4.0 Międzynarodowa*
dc.rights.licenceCC-BY-NC-SA
dc.rights.urihttp://creativecommons.org/licenses/by-nc-sa/4.0/legalcode.pl*
dc.share.typeotwarte czasopismo
dc.subject.enendolymphatic sac tumourpl
dc.subject.enELSTpl
dc.subject.entemporal bonepl
dc.subject.envon Hippel-Lindau diseasepl
dc.subtypeArticlepl
dc.titleEndolymphatic sac tumour (ELST). Case report of a rare tumour of the temporal bone, presenting as a mass in a cerebello-pontine anglepl
dc.title.journalFolia Neuropathologicapl
dc.typeJournalArticlepl
dspace.entity.typePublication
cris.lastimport.wos
2024-04-10T00:14:37Z
dc.abstract.enpl
Endolymphatic sac tumour (ELST) is a primary low-grade, locally invasive adenocarcinoma of the endolymphatic sac, characterized by the proliferation of cuboidal cells forming a papillotubular pattern and colloid-filled cysts. Rare in the general population, it coincides significantly with the presence of von Hippel-Lindau disease. The natural history, mechanisms underlying the early symptoms, anatomical origin of ELST and optimal timing of their treatment are unknown. In this study, we report a Polish male patient with sporadic ELST (without a family history of VHL disease) along with a review of literature. The light microscopic and immunohistochemical features as well as clinical presentation were typical of ELST.
dc.affiliationpl
Wydział Lekarski : Zakład Patomorfologii Klinicznej i Doświadczalnej
dc.affiliationpl
Wydział Lekarski : Zakład Neuropatologii
dc.cm.date
2020-01-07
dc.cm.id
58981
dc.contributor.authorpl
Czopek, Jacek - 129116
dc.contributor.authorpl
Waśko, Marcin
dc.contributor.authorpl
Adamek, Dariusz - 128411
dc.date.accessioned
2020-01-17T07:51:52Z
dc.date.available
2020-01-17T07:51:52Z
dc.date.issuedpl
2013
dc.date.openaccess
0
dc.description.accesstime
w momencie opublikowania
dc.description.numberpl
2
dc.description.physicalpl
164-168
dc.description.pointspl
15
dc.description.version
ostateczna wersja wydawcy
dc.description.volumepl
51
dc.identifier.doipl
10.5114/fn.2013.35960
dc.identifier.eissnpl
1509-572X
dc.identifier.issnpl
1641-4640
dc.identifier.projectpl
ROD UJ / OP
dc.identifier.uri
https://ruj.uj.edu.pl/xmlui/handle/item/131556
dc.languagepl
eng
dc.language.containerpl
eng
dc.rights*
Udzielam licencji. Uznanie autorstwa - Użycie niekomercyjne - Na tych samych warunkach 4.0 Międzynarodowa
dc.rights.licence
CC-BY-NC-SA
dc.rights.uri*
http://creativecommons.org/licenses/by-nc-sa/4.0/legalcode.pl
dc.share.type
otwarte czasopismo
dc.subject.enpl
endolymphatic sac tumour
dc.subject.enpl
ELST
dc.subject.enpl
temporal bone
dc.subject.enpl
von Hippel-Lindau disease
dc.subtypepl
Article
dc.titlepl
Endolymphatic sac tumour (ELST). Case report of a rare tumour of the temporal bone, presenting as a mass in a cerebello-pontine angle
dc.title.journalpl
Folia Neuropathologica
dc.typepl
JournalArticle
dspace.entity.type
Publication
Affiliations

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